Review and Prospect of Clinical Research on Idiopathic Interstitial Pneumonias

Idiopathic interstitial pneumonias (ⅡPs) are a group of heterogeneous diffuse parenchymal lung diseases of unknown etiology, which mainly involve the interstitium of the lung. With the deepening of research, the classification and treatment of ⅡPs have gone through a process of continuous evolution。This article reviewed the changes in the classification of ⅡPs, the evolution of the concept and definition of acute exacerbation of idiopathic pulmonary fibrosis, and the background and latest progress in the treatment plan at different periods of IPF.We also prospected the classification, diagnosis, and treatment of ⅡPs in the future.