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肥厚型心肌病心脏性猝死的高危因素及预防

潘玉惠 桑文涛 边圆 徐峰

潘玉惠, 桑文涛, 边圆, 徐峰. 肥厚型心肌病心脏性猝死的高危因素及预防[J]. 协和医学杂志. doi: 10.12290/xhyxzz.2022-0627
引用本文: 潘玉惠, 桑文涛, 边圆, 徐峰. 肥厚型心肌病心脏性猝死的高危因素及预防[J]. 协和医学杂志. doi: 10.12290/xhyxzz.2022-0627
PAN Yuhui, SANG Wentao, BIAN Yuan, XU Feng. Sudden Cardiac Death in Hypertrophic Cardiomyopathy: Hig-risk Factors and Prevention[J]. Medical Journal of Peking Union Medical College Hospital. doi: 10.12290/xhyxzz.2022-0627
Citation: PAN Yuhui, SANG Wentao, BIAN Yuan, XU Feng. Sudden Cardiac Death in Hypertrophic Cardiomyopathy: Hig-risk Factors and Prevention[J]. Medical Journal of Peking Union Medical College Hospital. doi: 10.12290/xhyxzz.2022-0627

肥厚型心肌病心脏性猝死的高危因素及预防

doi: 10.12290/xhyxzz.2022-0627
基金项目: 

泰山学者攀登计划专家建设工程专项经费(tspd20181220)

山东省重点研发计划(2021ZLGX02)

国家重点研发计划(2020YFC1512700)

详细信息
    通讯作者:

    徐峰,E-mail:xufengsdu@126.com;边圆,E-mail:bianyuan@sdu.edu.cn

    徐峰,E-mail:xufengsdu@126.com;边圆,E-mail:bianyuan@sdu.edu.cn

  • 中图分类号: R459.7

Sudden Cardiac Death in Hypertrophic Cardiomyopathy: Hig-risk Factors and Prevention

  • 摘要: 肥厚型心肌病(hypertrophic Cardiomyopathy,HCM)是最常见的遗传性心肌病之一,心脏性猝死是其最严重的结局。及早识别、早期预防可推迟或避免心脏骤停的发生,因此,明确HCM的猝死高危因素对于患者预后至关重要。目前HCM公认的高危因素主要包括猝死家族史、非持续性室性心动过速、严重左心室肥厚、不明原因晕厥、左心室射血分数<50%的终末期肥厚型心肌病、任何大小的左心室心尖室壁瘤以及广泛晚期钆增强等,预防措施主要包括药物治疗、外科室间隔心肌切除术、室间隔心肌酒精消融术和植入式心脏复律除颤器等。本文围绕识别肥厚型心肌病引发心脏性猝死的高危因素以及预防策略,就HCM预防、诊断、治疗方面的最新研究进展作一综述,以期为改善HCM患者的临床结局提供指导。
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出版历程
  • 收稿日期:  2022-10-31
  • 录用日期:  2023-02-07
  • 网络出版日期:  2023-02-23

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