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摘要: 本文报道一例先天性阴道下段闭锁伴膀胱阴道瘘, 从临床症状、检查、诊断和处理方法等方面介绍该病特点, 并通过文献回顾加深临床医师对此类泌尿生殖系统畸形的认识。当青春期后出现周期性血尿而无阴道月经出血时, 应怀疑阴道闭锁合并先天性膀胱阴道瘘的可能。影像学检查和膀胱镜是重要的辅助诊断手段。手术切开闭锁的阴道、引流积血并修补瘘道是唯一的治疗手段。Abstract: We reported one patient with rare malformation, congenital lower vaginal atresia with vesico-vaginal fistula, and introduced the characteristics of this case encompassing clinical symptoms, examinations, diagnosis and management. Meanwhile, we reviewed previously reported similar cases to help clinical physicians better understand urogenital system malformation. When periodic hematuria without vaginal menstrual bleeding occurs in puberty, congenital vaginal atresia with vesico-vaginal fistula should be suspected. Imaging examinations and cystoscopy are important adjuvant diagnostic methods. The only treatment of this disease is surgical incision of the vaginal atresia for drainage and repair of the fistula tract.
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Key words:
- congenital vaginal atresia /
- vesico-vaginal fistula /
- hematuria
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