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摘要: IgG4相关性疾病(IgG4-related disease, IgG4-RD)是累及多器官或组织的慢性进行性自身免疫性疾病, 其病理为受累脏器被淋巴细胞和IgG4阳性的浆细胞浸润, 肺部表现多样。本文报道了一例以咳嗽、气短起病的IgG4-RD, 有肺、纵膈淋巴结、左颌下淋巴结、腹膜后、脾门、胃粘膜、皮肤受累, 其肺野内病变表现为弥漫微结节, 激素治疗后完全消失。Abstract: IgG4-related disease(IgG4-RD) is a chronic autoimmune disease implicating multiple organs and tissues. Its pathological characteristics are infiltration of lymphocytes and IgG4-positive plasma cells in the implicated organs. Pulmonary involvement reportedly varies. Here we reported a case of IgG4-RD with the onset of cough and dyspnea, presenting with multiple lesions. The pulmonary involvement was manifested as diffuse nodules in lungs that dissolved after glucocorticoid therapy.
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Key words:
- IgG4-related disease /
- pulmonary nodule /
- glucocorticoid
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